Extramedullary Hematopoiesis in a Patient with Beta Thalassemia: A Rare Case Report

CASE REPORT
Mohammed Saad Alqahtani

 
For citation: Alqahtani MS. Extramedullary Hematopoiesis in a Patient with Beta Thalassemia: A Rare Case Report. International Journal of Biomedicine. 2024;14(2):345-347. doi:10.21103/Article14(2)_CR3
 
Originally published June 5, 2024
 

Abstract: 

Extramedullary hematopoiesis (EMH) is a rare disorder, defined as the appearance of hematopoietic elements outside the bone marrow or peripheral blood due to ineffective erythropoiesis or inadequate bone marrow activity in a variety of hematological diseases. EMH often manifests as hemopoietic masses in a variety of normal and abnormal bodily sites. We present a 21-year-old man with a medical history of beta thalassemia since he was nine months old. The primary clinical symptom was mild abdominal pain. In this case, we describe a rare instance of small bowel obstruction due to EMH and portal hypertension. Surgery solved the clinical problems, and the patient was discharged home.

Keywords: 
thalassemia • small bowel obstruction • extramedullary hematopoiesis
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Received April 2, 2024.
Accepted May 13, 2024.
©2024 International Medical Research and Development Corporation.