Frantz Tumor, a Rare Indolent Pancreatic Neoplasm Entity: A Case Report and Brief Review

CASE REPORT
Faton T. Hoxha, Rrustem Musa, Shemsedin Hashani, Reshat Mati, Arb F. Hoxha, Nart F. Hoxha, Hasime Terziqi, Antigona Ukëhaxhaj

 
For citation: Hoxha FT, Musa R, Hashani S, Mati R, Hoxha AF, Hoxha NF, Terziqi H, Ukëhaxhaj A. Frantz Tumor, a Rare Indolent Pancreatic Neoplasm Entity: A Case Report and Brief Review. International Journal of Biomedicine. 2024;14(1):175-178. doi:10.21103/Article14(1)_CR5
 
Originally published March 1, 2024

Abstract: 

Solid pseudopapillary neoplasm (SPN) of the pancreas, also known as Frantz tumor, is an uncommon tumor with indolent clinical features that primarily affects young women. We are presenting a 27-year-old Caucasian female with an accidental finding with pancreatic SPN who underwent complete resection of the tumor using a distal pancreatectomy and splenectomy procedure. Immunohistochemistry revealed low-grade pancreatic SPN. Despite the rare appearance, it should be considered in the differential diagnosis of a young female with a large pancreatic mass.

Keywords: 
Frantz tumor • solid pseudopapillary neoplasm • pancreas • distal pancreatectomy
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Received December 12, 2023.
Accepted January 20, 2024.
©2024 International Medical Research and Development Corporation.